Hyperacusis as the initial presentation of Creutzfeldt-Jakob disease

Hyperacusis as the initial presentation of Creutzfeldt-Jakob disease

Case. A 52-year-old man with diabetes presented with 1 month of hyperacusis and trouble discerning noises, including speech and music. He reported that all sounds, both complex and simple, seemed “jarring” and unfamiliar. He denied tinnitus, falls, or imbalance. Over the ensuing 3 months he developed diffuse myalgias and neck pain. Medical and neurologic examination was normal as was audiometry...

Hearing loss as the initial presentation of Creutzfeldt-Jakob disease.

Creutzfeldt-Jakob disease is a rare type of spongiform encephalopathy. Affected patients present with constitutional symptoms, which progress to severe mental deterioration and movement disorders. Dizziness is the most common early otologic symptom. Few reports in the literature describe patients with Creutzfeldt-Jakob disease who present with sudden-onset hearing loss as their primary symptom ...

Herpes simplex encephalitis as an initial presentation of Creutzfeldt-Jakob disease.

Sporadic Creutzfeldt-Jakob disease with unusual initial presentation as posterior reversible encephalopathy syndrome: a case report

BACKGROUND Creutzfeldt - Jakob disease (CJD) is a rapidly progressive and fatal neurodegenerative prion disease. MRI findings are included in diagnostic criteria for probable CJD, giving a sensitivity and specificity more than 90%, but the atypical radiological presentations in the early stage of the disease could cause the diagnostic difficulties. CJD can be definitively diagnosed by histopath...

Creutzfeldt-Jakob disease: A case report

Background: Creutzfeldt-Jakob disease (CJD) as a life-threatening neurodegenerative disorder is not usually diagnosed in early stages of the disease because of a variety in its clinical manifestations. This study aimed to present a middle-aged woman with psychiatric symptoms who ultimately was diagnosed as a CJD case. Case presentation: This 48-year-old woman had progressive symptoms of depres...